Mitochondrial Disorders in Neurology 2

Content: 
Edited by
Page iii

Copyright
Page iv

Contributing Authors
Pages vii-viii

Series Preface
Page ix
Arthur K. Asbury, Anthony H.V. Schapira

In Memory of C. David Marsden
Page xi
Arthur K. Asbury, Anthony H.V. Schapira

Preface
Pages xiii-xv
Anthony H.V. Schapira, Salvatore DiMauro

Colour Plates
Pages CP1-CP4

Chapter 1 Structure and Function of the Mitochondrial Oxidative Phosphorylation System Original Research Article
Pages 1-34
Jan-Willem Taanman, Siôn Llewelyn Williams

Chapter 2 Clinical Features of the Mitochondrial Encephalomyopathies Original Research Article
Pages 35-68
Paul E. Hart, Darryl C. De Vivo, Anthony H.V. Schapira

Chapter 3 Molecular Genetic Basis of the Mitochondrial Encephalomyopathies Original Research Article
Pages 69-113
Eric A. Schon, Michio Hirano, Salvatore DiMauro

Chapter 4 Leber's Hereditary Optic Neuropathy Original Research Article
Pages 115-142
Valerio Carelli

Chapter 5 Mitochondrial Abnormalities in Neurodegenerative Disorders Original Research Article
Pages 143-174
Sarah J. Tabrizi, Anthony H.V. Schapira

Chapter 6 Pathophysiology of Mitochondrial Disease as Illuminated by Animal Models Original Research Article
Pages 175-212
Douglas C. Wallace

Chapter 7 Current and Future Prospects for the Treatment of Mitochondrial Disorders Original Research Article
Pages 213-227
Robert W. Taylor, Douglass M. Turnbull

Chapter 8 Defects of Pyruvate Dehydrogenase and Intermediary Metabolism Original Research Article
Pages 229-256
Garry Kenneth Brown

Chapter 9 Inherited Disorders of Mitochondrial Fatty Acid β-Oxidation Original Research Article
Pages 257-297
R.J.A. Wanders, M. Duran, F.A. Wijburg

Index
Pages 299-304