Clinical Neurophysiology of Motor Neuron Diseases

Content: 
Volume Editor
Page iii

Copyright
Page iv

Dedication
Page v

Foreword
Page vii

List of Contributors
Pages ix-xii

Contents
Pages xiii-xv

Overview Original Research Article
Pages 1-3
Andrew Eisen

Comparative anatomy of the motor system: differences in the organization of corticospinal control in different species Original Research Article
Pages 7-25
Roger Lemon, James Griffiths

Developmental aspects of corticospinal projections Original Research Article
Pages 27-57
J.A. Eyre

Principles of corticospinal system organization and function Original Research Article
Pages 59-96
Paul D. Cheney, Abderraouf Belhaj-Saı̈f, Marie-Hélène Boudrias

Molecular mechanisms regulating motor neuron development and degeneration Original Research Article
Pages 97-118
T.J. Kilpatrick, N. Tubridy

Physiology of the motor neuron and the motor unit Original Research Article
Pages 119-147
C.J. Heckman, Roger M. Enoka

Cytopathology of the motor neuron Original Research Article
Pages 149-167
Paul G. Ince, Stephen B. Wharton

Genetics of amyotrophic lateral sclerosis Original Research Article
Pages 169-186
M. Dewil, P.M. Andersen, L. Van Den Bosch, W. Robberecht

Neuroimaging in amyotrophic lateral sclerosis Original Research Article
Pages 187-200
Giancarlo Comi, Letizia Leocani

Animal models of motor neuron death Original Research Article
Pages 201-218
Jean-Pierre Julien

Needle electromyography Original Research Article
Pages 221-240
Jasper R. Daube, Eric J. Sorenson

Peripheral nerve conduction studies and neuromuscular junction testing Original Research Article
Pages 241-270
Jun Kimura

Motor unit number estimates Original Research Article
Pages 271-281
Jeremy M. Shefner

Magnetic stimulation and central conduction time Original Research Article
Pages 283-293
K.R. Mills

Evoked potentials in amyotrophic lateral sclerosis Original Research Article
Pages 295-303
Reinhard Dengler, Klaus Krampfl

The triple stimulation technique Original Research Article
Pages 305-315
Kai M. Rösler, Michel R. Magistris

Cortical threshold and excitability measurements Original Research Article
Pages 317-335
Ulf Ziemann

Spinal and long-latency reflexes Original Research Article
Pages 337-348
Tihomir V. Ilic, Günther Deuschl

Single unit recordings – peristimulus time histograms (PSTHs) Original Research Article
Pages 349-358
Markus Weber

Threshold electrotonus and the assessment of nerve excitability in amyotrophic lateral sclerosis Original Research Article
Pages 359-366
Matthew C. Kiernan, David Burke

Other forms of spinal muscular atrophies Original Research Article
Pages 369-386
Marianne de Visser, Hessel Franssen

Arthrogryposis multiplex and related congenital disorders Original Research Article
Pages 387-401
Judith G. Hall

Spinobulbar muscular atrophy (Kennedy\'s disease) Original Research Article
Pages 403-417
Jean-Marc Gallo

Late muscular sequelae after poliomyelitis Original Research Article
Pages 419-435
Erik Stålberg

Toxic motor neuronopathies and neuropathies Original Research Article
Pages 437-450
Shannon L. Venance, Michael J. Strong

Motor neuron disorders with other diseases and exposures Original Research Article
Pages 451-466
J.D. Mitchell, A.M. Beaumont

Classic Charcot amyotrophic lateral sclerosis Original Research Article
Pages 469-485
Andrew Eisen, Charles Krieger

Electrophysiological evaluation of oropharyngeal dysphagia in ALS Original Research Article
Pages 487-512
Cumhur Ertekin

Electrodiagnostic assessment of respiratory dysfunction in motor neuron disease Original Research Article
Pages 513-528
Mamede De Carvalho

Assessment of autonomic function in motor neuron diseases Original Research Article
Pages 529-541
P. Liam Oey

Neurophysiology of hereditary amyotrophic lateral sclerosis Original Research Article
Pages 543-562
Heather G. Stewart, Peter M. Andersen

Autosomal recessive juvenile amyotrophic lateral sclerosis Original Research Article
Pages 563-567
Fayçal Hentati

Paraneoplastic motor neuron disease Original Research Article
Pages 569-582
Eduardo Nobile-Orazio, Alberto Cappellari

Multifocal motor neuropathy Original Research Article
Pages 583-604
Ryuji Kaji

Focal amyotrophies of the upper and lower limbs Original Research Article
Pages 605-619
Antonino Uncini, Antonio Di Muzio

Primary lateral sclerosis Original Research Article
Pages 623-632
Nadine Le Forestier, Vincent Meininger

Hereditary spastic paraplegia Original Research Article
Pages 633-653
Hatem El-Shanti

Hereditary ataxias Original Research Article
Pages 655-673
Thomas Klockgether, Michael Abele

Konzo Original Research Article
Pages 675-686
Karin Edebol Eeg-Olofsson, Desiré Tshala-Katumbay

Application of clinical neurophysiology to clinical trials involving motor neuron diseases Original Research Article
Pages 689-697
Mark B. Bromberg

The role of clinical neurophysiology inmotor neuron diseases: where next? Original Research Article
Pages 701-711
Michael Swash

Index
Pages 713-724