Branched-Chain Amino Acids, Part B

Content: 
Contributors to volume 324
Pages xi-xiv

Preface
Page xv
Robert A Harris, John R Sokatch

Volumes in series
Pages xvii-xxxv

Synthesis and gas chromatography/mass spectrometry analysis of stereoisomers of 2-hydroxy-3-methylpentanoic acid Original Research Article
Pages 3-10
Orval A Mamer

Analysis of intracellular metabolites as tool for studying branched-chain amino acid biosynthesis and its inhibition in bacteria Original Research Article
Pages 10-23
Sabine Epelbaum, David M Chipman, Ze\'ev Barak

Determination of branched-chain l-amino-acid aminotransferase activity Original Research Article
Pages 23-32
Peter Schadewaldt

Analysis of (S)- and (R)-3-methyl-2-oxopentanoate enantiomorphs in body fluids Original Research Article
Pages 33-39
Peter Schadewaldt

Spectrophotometric assay for measuring branched-chain amino acids Original Research Article
Pages 40-47
Philip R Beckett

Determination of branched-chain О±-keto acid dehydrogenase activity state and branched-chain О±-keto acid dehydrogenase kinase activity and protein in mammalian tissues
Pages 48-62
Naoya Nakai, Rumi Kobayashi, Kirill M Popov, Robert A Harris, Yoshiharu Shimomura

Simultaneous quantification of plasma levels of О±-ketoisocaproate and leucine by gas chromatography-mass spectrometry Original Research Article
Pages 62-73
Marzia Galli Kienle, Fulvio Magni

Synthesis of methacrylyl-CoA and (R)- and (S)-3-hydroxyisobutyryl-CoA Original Research Article
Pages 73-79
John W Hawes, Edwin T Harper

Pathways of leucine and valine catabolism in yeast Original Research Article
Pages 80-92
J Richard Dickinson

Isolation of subunits of acetohydroxy acid synthase isozyme III and reconstitution of holoenzyme Original Research Article
Pages 95-103
Maria Vyazmensky, Tsiona Elkayam, David M Chipman, Ze\'ev Barak

Branched-chain amino-acid aminotransferase of Escherichia coli Original Research Article
Pages 103-113
Hiroyuki Kagamiyama, Hideyuki Hayashi

Purification of sodium-coupled branched-chain amino acid carrier of Pseudomonas aeruginosa Original Research Article
Pages 114-121
Yoshihiko Uratani, Toshimitsu Hoshino

Reconstitution of Pseudomonas aeruginosa high-affinity branched-chain amino acid transport system
Pages 122-129
Toshimitsu Hoshino, Yoshihiko Uratani

Purification of Pseudomonas putida branched-chain keto acid dehydrogenase E1 component
Pages 129-138
Kathryn L Hester, Jinhe Luo, John R Sokatch

Pseudomonas mevalonii 3-hydroxy-3methylglutaryl-CoA lyase Original Research Article
Pages 139-149
Henry M Miziorko, Chakravarthy Narasimhan

Human 3-hydroxy-3-methylglutaryl-CoA lyase Original Research Article
Pages 150-161
Henry M Miziorko, Chakravarthy Narasimhan, Jacqueline R Roberts

Branched-chain О±-keto acid dehydrogenase kinase Original Research Article
Pages 162-178
Kirill M Popov, Yoshiharu Shimomura, John W Hawes, Robert A Harris

Expression of E1 component of human branched-chain О±-keto acid dehydrogenase complex in Escherichia coli by cotransformation with Chaperonins GroEL and GroES Original Research Article
Pages 179-191
R.Max Wynn, James R Davie, Jiu-Li Song, Jacinta L Chuang, David T Chuang

Production of recombinant mammalian holo-E2 and E3 and reconstitution of functional branched-chain О±-keto acid dehydrogenase complex with recombinant E1 Original Research Article
Pages 192-200
Jacinta L Chuang, James R Davie, R.Max Wynn, David T Chuang

Production of recombinant E1 component of branched-chain О±-keto acid dehydrogenase complex Original Research Article
Pages 201-207
John W Hawes, Yu Zhao, Kirill M Popov, Yoshiharu Shimomura, Robert A Harris

Mammalian methylmalonate-semialdehyde dehydrogenase Original Research Article
Pages 207-218
Natalia Y Kedishvili, Gary W Goodwin, Kirill M Popov, Robert A Harris

Mammalian 3-hydroxyisobutyrate dehydrogenase Original Research Article
Pages 218-228
John W Hawes, David W Crabb, Rebecca J Chan, Paul M Rougraff, Ralph Paxton, Robert A Harris

3-Hydroxyisobutyryl-CoA hydrolase Original Research Article
Pages 229-240
Yoshiharu Shimomura, Taro Murakami, Naoya Nakai, Boli Huang, John W Hawes, Robert A Harris

Mammalian branched-chain acyl-CoA dehydrogenases: Molecular cloning and characterization of recombinant enzymes Original Research Article
Pages 241-258
Jerry Vockley, Al-Walid A Mohsen, Barbara Binzak, Jan Willard, Abdul Fauq

3-Hydroxy-3-methylglutaryl-CoA reductase Original Research Article
Pages 259-280
Victor W Rodwell, Michael J Beach, Kenneth M Bischoff, Daniel A Bochar, Bryant G Darnay, Jon A Friesen, John F Gill, Matua Hedl, Tuajuanda Jordan-Starck, Peter J Kennelly, Dongyul Kim, Yuli Wang

Characterization of 3-methylcrotonyl-CoA carboxylase from plants Original Research Article
Pages 280-292
Eve Syrkin Wurtele, Basil J Nikolau

Purification of d-hydroxyisovalerate dehydrogenase from Fusarium sambucinum Original Research Article
Pages 293-301
Rainer Zocher

[28] Purification and characterization of recombinant 3-Isopropylmalate dehydrogenases from thermus thermophilus and other microorganisms Original Research Article
Pages 301-322
Yoko Hayashi-Iwasaki, Tairo Oshima

[29] Wild-type and hexahistidine-tagged derivatives of leucine-responsive regulatory protein from escherichia coli Original Research Article
Pages 322-329
Rowena G Matthews, Yuhai Cui, Devorah Friedberg, Joseph M Calvo

Purification of branched-chain keto acid dehydrogenase regulator from Pseudomonas putida Original Research Article
Pages 329-335
Kunapuli T. Madhusudhan, John R. Sokatch

Mitochondrial import of mammalian branched-chain О±-keto acid dehydrogenase complex subunits Original Research Article
Pages 336-342
Dean J Danner

Cloning, expression, and purification of mammalian 4-hydroxyphenylpyruvate dioxygenase/О±-ketoisocaproate dioxygenase Original Research Article
Pages 342-355
Nicholas P Crouch, Meng-Hues Lee, Teresa Iturriagagoitia-Bueno, Colin H MacKinnon

Mammalian branched-chain aminotransferases Original Research Article
Pages 355-365
Myra E Conway, Susan M Hutson

Branched-chain-amino-acid transaminases of yeast Saccharomyces cerevisiae Original Research Article
Pages 365-375
Corinna Prohl, Gyula Kispal, Roland Lill

Purification, properties, and sequencing of aminoisobutyrate aminotransferases from rat liver Original Research Article
Pages 376-389
Nanaya Tamaki, Shigeko Fujimoto Sakata, Koichi Matsuda

Branched-chain keto acid dehydrogenase of yeast Original Research Article
Pages 389-398
J Richard Dickinson

ОІ-Alanine synthase, an enzyme involved in catabolism of uracil and thymine Original Research Article
Pages 399-410
Thomas W Traut

Diagnosis and mutational analysis of maple syrup urine disease using cell cultures Original Research Article
Pages 413-423
Jacinta L Chuang, David T Chuang

Detection of gene defects in branched-chain amino acid metabolism by tandem mass spectrometry of carnitine esters produced by cultured fibroblasts Original Research Article
Pages 424-431
Charles R Roe, Diane S Roe

Molecular and enzymatic methods for detection of genetic defects in distal pathways of branched-chain amino acid metabolism Original Research Article
Pages 432-453
K Michael Gibson, Magdalena Ugarte, Toshiyuki Fukao, Grant A Mitchell

Genetic defects in E3 component of О±-keto acid dehydrogenase complexes Original Research Article
Pages 453-464
Mulchand S Patel, Young Soo Hong, Douglas S Kerr

Targeting E3 component of О±-keto acid dehydrogenase complexes Original Research Article
Pages 465-476
Mark T Johnson, Hsin-Sheng Yang, Mulchand S Patel

Regulation of expression of branched-chain О±-keto acid dehydrogenase subunits in permanent cell lines Original Research Article
Pages 479-490
Jeffrey M Chinsky, Paul A Costeas

Expression of murine branched-chain О±-keto acid dehydrogenase kinase Original Research Article
Pages 491-497
Christopher B Doering, Dean J Danner

Regulation of branched-chain О±-keto acid dehydrogenase kinase gene expression by glucocorticoids in hepatoma cells and rat liver Original Research Article
Pages 498-511
Yi-Shuian Huang, David T Chuang

Author index
Pages 513-533

Subject index
Pages 535-550