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ویرایش: نویسندگان: Lan Zhou , Dennis K. Burns, Chunyu Cai سری: ISBN (شابک) : 9783030256821 ناشر: Springer International Publishing سال نشر: 2020 تعداد صفحات: زبان: English فرمت فایل : EPUB (درصورت درخواست کاربر به PDF، EPUB یا AZW3 تبدیل می شود) حجم فایل: 219 Mb
در صورت تبدیل فایل کتاب A Case-Based Guide to Neuromuscular Pathology به فرمت های PDF، EPUB، AZW3، MOBI و یا DJVU می توانید به پشتیبان اطلاع دهید تا فایل مورد نظر را تبدیل نمایند.
توجه داشته باشید کتاب راهنمای موردی برای آسیب شناسی عصبی عضلانی نسخه زبان اصلی می باشد و کتاب ترجمه شده به فارسی نمی باشد. وبسایت اینترنشنال لایبرری ارائه دهنده کتاب های زبان اصلی می باشد و هیچ گونه کتاب ترجمه شده یا نوشته شده به فارسی را ارائه نمی دهد.
این کتاب راهنمای عملی در زمینه آسیب شناسی عصبی عضلانی شامل بیوپسی عضلانی، عصب محیطی و پوست با تفسیر بیوپسی ارائه می دهد. این کتاب که به سه بخش تقسیم می شود، با فصل های مقدماتی شروع می شود که نشانه ها و روش های بیوپسی عضله، عصب و پوست، بافت شناسی عضلانی و اعصاب طبیعی و آسیب شناسی عضلانی و عصبی مشترک را بررسی می کند. 28 فصل مورد میوپاتی در قسمت 2 و 11 فصل مورد نوروپاتی در قسمت 3 ویژگی های بالینی و پاتولوژیک بسیاری از بیماری های عصبی عضلانی را نشان می دهد، نشانه ها و کاربردهای بیوپسی را نشان می دهد، در مورد تشخیص افتراقی بالینی و پاتولوژیک بحث می کند، مدیریت بیماری فردی را به روز می کند، و خلاصه می کند. مرواریدهای بالینی و پاتولوژی مربوط به هر مورد. راهنمای موردی برای آسیب شناسی عصبی عضلانی به عنوان یک مرجع ضروری برای متخصصان مغز و اعصاب و آسیب شناسان به دنبال درک مفید بودن بیوپسی عضله، عصب و پوست عمل می کند. این کتاب همچنین به دستیاران مغز و اعصاب، همراهان عصبی-عضلانی و همکاران نوروپاتولوژی در آماده شدن برای سؤالات مربوط به آسیب شناسی عضلانی و اعصاب در امتحانات ضمن خدمت و هیئت مدیره کمک می کند.
This book provides a practical guide to the field of neuromuscular pathology including muscle, peripheral nerve, and skin biopsies with biopsy interpretation. Divided into three parts, the book begins with introductory chapters that review muscle, nerve, and skin biopsy indications and procedures, normal muscle and nerve histology, and common muscle and nerve pathology. The 28 myopathy case chapters in Part 2 and 11 neuropathy case chapters in Part 3 illustrate the clinical and pathological features of many neuromuscular diseases, demonstrate the indications and utilities of biopsies, discuss clinical and pathological differential diagnosis, update the individual disease management, and summarize pertinent clinical and pathology pearls for each case. A Case-Based Guide to Neuromuscular Pathology will function as an indispensable reference for neurologists and pathologists looking to understand the utility of muscle, nerve, and skin biopsies. This book will also aid neurology residents, neuromuscular fellows and neuropathology fellows in preparing for questions related to the muscle and nerve pathology in their in-service and board exams.
Preface Contents Contributors Part I: Introduction to Neuromuscular Pathology Evaluation Chapter 1: Skeletal Muscle Biopsy Evaluation Introduction Muscle Biopsy Acquisition Initial Processing and Sectioning of Skeletal Muscle Biopsies Routine Histological Stains Non-enzymatic Stains (Frozen Sections) Enzyme Histochemical Stains (Frozen Sections) Non-enzymatic Staining of Fixed Skeletal Muscle (Paraffin Sections) Immunohistochemical Stains Electron Microscopy Interpretation of the Biopsy Myofiber Atrophy and Hypertrophy Myofiber Degeneration, Necrosis and Regeneration Changes in the Location and Appearance of Myofiber Nuclei Sarcoplasmic Abnormalities Changes in Connective Tissue Cellular Infiltrates Vascular Changes Artifacts in Skeletal Muscle Biopsies References Chapter 2: Peripheral Nerve Biopsy Evaluation Introduction Nerve Biopsy Acquisition Specimen Processing Procedure Routine Stains and Utilities Hematoxylin and Eosin (H&E) Congo Red Stain Toluidine Blue Stained Plastic Sections Electron Microscopy (EM) Teased Fiber Analysis Special Stains and Utilities Immunostains References Chapter 3: Skin Biopsy with Cutaneous Nerve Fiber Evaluation Introduction Skin Biopsy Procedure Skin Biopsy Specimen Processing Small Cutaneous Nerve Fiber Evaluation Intraepidermal Nerve Fiber Density Evaluation Intraepidermal Nerve Fiber Morphology Evaluation Cutaneous Autonomic Nerve Fiber Evaluation Limited Usefulness of Skin Biopsy in Evaluation of SFN Etiologies References Part II: Myopathy Cases Chapter 4: A 20-Year-Old Man with Acute Multi-organ Failure and Rhabdomyolysis History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion References Chapter 5: A 45-Year-Old Woman with Proximal Limb Weakness and Skin Peeling on Fingertips History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 6: A 75-Year-Old Man with Slowly Progressive Leg and Hand Weakness History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 7: A 53-Year-Old Woman with Proximal Limb Weakness and Marked CK Elevation History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 8: A 61-Year-Old Woman with Progressive Distal Limb and Deltoid Muscle Weakness History Physical Examination Investigations Muscle Biopsy Findings Additional Investigations After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 9: A 63-Year-Old Woman with Debilitating Muscle Pain History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 10: A 33-Year-Old Woman with Pain and Swelling in the Right Calf and Persistent Fever History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 11: A 28-Year-Old Woman with Proximal Limb Weakness and Scapular Winging History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 12: A 52-Year-Old Man with Proximal Limb Weakness and Hand Stiffness History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 13: A 51-Year-Old Woman with Long-Standing Exercise Intolerance History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 14: A 37-Year-Old Woman with Leg Weakness and CK Elevation History Physical Examination Investigations Muscle Biopsy Findings Additional Investigations After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 15: A 25-Year-Old Woman with Droopy Eyelids and Double Vision History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 16: A 58-Year-Old Man with Hypercapnic Respiratory Failure History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 17: A 65-Year-Old Man with Asymmetrical Leg Weakness and Foot Tingling History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 18: A 40-Year-Old Man with Muscle Pain and Fatigue History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 19: A 42-Year-Old Woman with Progressive Limb Weakness and Breathing Difficulty History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 20: A 49-Year-Old Man with Limb Weakness and Painful Skin Lesions History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 21: A 54-Year-Old Man with Progressive Lower Limb Weakness and CK Elevation History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 22: A 63-Year-Old Man with Progressive Limb Weakness and Slurred Speech History Physical Examination Investigations Muscle and Nerve Biopsy Findings Additional Investigation After the Muscle and Nerve Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 23: A 6-Year-Old Girl with Muscle Pain and Swelling in the Thighs History Physical Examination Investigations Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 24: A 4-Year-Old Boy with Progressive Weakness, Difficulty Walking and Running, and Increased Falls History Physical Examination Investigations Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 25: A 2-Year-Old Girl with Hypotonia Since Birth and Delayed Motor and Speech Development History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 26: An 8-year-old boy with delayed motor milestones and proximal leg muscle weakness History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 27: A 6-Year-Old-Boy with Proximal Leg Muscle Weakness and Facial Weakness History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-Up Discussion Pearls References Chapter 28: A 6-Week-Old Boy with Neonatal Hypotonia and Feeding and Respiratory Difficulties History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 29: A 6-Year-Old Boy with Respiratory and Feeding Difficulties at Birth, Delayed Gross Motor Milestones, and Facial and Proximal Lower Limb Weakness History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 30: A 12-Year-Old Girl with a 2-Year History of Progressive Limb Weakness and Difficulties with Exercise History Physical Examination Investigations Muscle Biopsy Findings Additional Investigation After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 31: A 3-Month-Old Boy with Generalized Hypotonia, Weakness, Pneumonia and Respiratory Failure History Physical Examination Investigations Muscle Biopsy Findings Investigations After the Muscle Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Part III: Neuropathy Cases Chapter 32: A 59-Year-Old Woman with Subacute Lower Limb Weakness and Painful Paresthesia History Physical Examination Investigations Nerve and Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 33: A 63-Year-Old Man with Nausea, Vomiting, Orthostatic Dizziness, and Distal Limb Paresthesia History Physical Examination Investigations Muscle and Nerve Biopsy Findings Additional Investigation After the Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 34: A 47-year-old woman with progressive numbness and weakness in the limbs History Physical Examination Investigations Nerve Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 35: A 65-Year-Old Woman with Acute Limb Weakness and Worsening of Paresthesia History Physical Examination Investigations Nerve and Muscle Biopsy Findings Additional Investigations After the Nerve and Muscle Biopsy Diagnoses Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 36: A 34-Year-Old Man with Right Hand and Left Foot Numbness History Physical Examination Investigations Nerve and Skin Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 37: A 64-Year-Old Woman with Progressive Pain, Numbness and Weakness in the Right Lower Limb History Physical Examination Investigations Nerve Lesion Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 38: A 68-Year-Old Man with Progressive Lower Limb Numbness and Weakness and Urinary Incontinence History Physical Examination Investigations Nerve and Muscle Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 39: A 53-Year-Old Woman with Pain, Burning, Tingling, and Numbness in the Distal Limbs History Physical Examination Investigations Skin Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 40: A 40-Year-Old Woman with Patchy Painful Paresthesia History Physical Examination Investigations Skin Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Chapter 41: A 39-Year-Old Woman with Intermittent Bilateral Foot and Leg Pain since Childhood History Physical Examination Investigations Skin Biopsy Findings Investigation After Obtaining the Skin Biopsy Diagnosis Final Diagnosis Patient Follow-up Discussion References Chapter 42: A 35-Year-Old Man with Pain and Numbness in the Left Lateral Thigh History Physical Examination Investigations Skin Biopsy Findings Final Diagnosis Patient Follow-up Discussion Pearls References Index of Cases Index