Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease

Front Matter....Pages i-xviii
Orphan Lung Diseases from Definition to Organisation of Care....Pages 1-3
The Challenges of Clinical Research in Orphan Diseases....Pages 5-15
Chronic Bronchiolitis in Adults....Pages 17-27
“Diffuse Bronchiectasis of Genetic Origin”....Pages 29-51
Allergic Bronchopulmonary Mycosis....Pages 53-71
Orphan Tracheopathies....Pages 73-89
Amyloidosis and the Respiratory Tract....Pages 91-111
Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss Syndrome): A Clinical and Therapeutic Approach....Pages 113-125
Granulomatosis with Polyangiitis (Wegener’s Granulomatosis)....Pages 127-153
Alveolar Hemorrhage....Pages 155-175
Pulmonary Involvement in Takayasu Arteritis and Behçet Disease....Pages 177-190
Pulmonary Vascular Manifestations of Hereditary Hemorrhagic Telangiectasia....Pages 191-200
Hepatopulmonary Syndrome....Pages 201-210
Non-langerhans Cell Histiocytosis-Including Erdheim-Chester Disease- and the Lung....Pages 211-226
Eosinophilic Pneumonia....Pages 227-251
Multiple Cystic Lung Diseases....Pages 253-270
Lymphangioleiomyomatosis....Pages 271-283
Pulmonary Alveolar Proteinosis....Pages 285-294
Exogenous Lipoid Pneumonia....Pages 295-303
Pulmonary Alveolar Microlithiasis....Pages 305-313
Pulmonary Fibrosis and the Many Faces of UIP....Pages 315-325
The Syndrome of Combined Pulmonary Fibrosis and Emphysema....Pages 327-347
Non-specific, Unclassifiable, and Rare Idiopathic Interstitial Pneumonia: Acute Interstitial Pneumonia, Respiratory Bronchiolitis Interstitial Pneumonia, Desquamative Interstitial Pneumonia, Nonspecific Interstitial Pneumonia....Pages 349-362
Organizing Pneumonias....Pages 363-378
Interstitial Lung Disease in Systemic Sclerosis....Pages 379-390
Interstitial Lung Disease in Connective Tissue Diseases Other Than Systemic Sclerosis....Pages 391-418
Interstitial Lung Disease in Undifferentiated Forms of Connective Tissue Disease....Pages 419-434
Pulmonary Langerhans Cell Histiocytosis and Smoking-Related Interstitial Lung Diseases....Pages 435-456
Rare Causes and the Spectrum of Hypersensitivity Pneumonitis....Pages 457-472
Chronic Beryllium Disease and Other Interstitial Lung Diseases of Occupational Origin....Pages 473-491
Lymphoproliferative Lung Disorders....Pages 493-515
Pulmonary Manifestations of Hematological Malignancies: Focus on Pulmonary Chronic Graft-Versus Host Disease....Pages 517-527
Pulmonary Hypertension in Orphan Lung Diseases....Pages 529-539
Rare and Emergent Drug-Induced and Iatrogenic Respiratory Conditions: A Guide to Their Recognition and Management....Pages 541-580
From Cancer Mimicking Orphan Lung Disease to Orphan Thoracic Oncology....Pages 581-596
Rare Diffuse Lung Diseases of Genetic Origin....Pages 597-609
Back Matter....Pages 611-625