32nd Hemophilia Symposium: Hamburg 2001

Front Matter....Pages II-XXIX
Front Matter....Pages 1-1
HIV Infection and Causes of Death in Patients with Hemophilia in Germany (Year 2000/2001 Survey)....Pages 3-12
Hemophilia 2001 — The Annual Survey of the Austrian Hemophilia Centers....Pages 13-16
Epidemiology of Hemophilia in Switzerland: A first Insight in the Data Base achieved by the Medical Committee of the Swiss Hemophilia Association....Pages 17-18
Overall Blood Supply Strategy with Regard to vCJD....Pages 19-22
Front Matter....Pages 23-23
11 novel Mutations in the Factor VIII encoding Gene lead to severe or moderate Hemophilia A....Pages 25-31
Molecular Analysis of Hemophilia B: »Greifswald Registry FIX Deficiency (Hemophilia B)«....Pages 35-48
Gly222Asp and Ser379Lys — Novel Factor X Gene Mutations in severe FX Deficiency — Greifswald Registry of Factor X congenital Deficiency....Pages 49-57
Hematopoietic Stem Cells as Targets for Gene Therapy of Hemophilia A....Pages 61-71
Adenovirus-mediated regulatable Expression of human Factor IX in vitro and in vivo ....Pages 72-80
Front Matter....Pages 81-81
Experiences with MRI Examination of the Joints of hemophilic Children....Pages 83-86
Rhenium-186 Hydroxyethylidenediphosphonate ( 186 Re HEDP) — A novel Treatment for hemophilic Arthropathies?....Pages 87-91
Monitoring of Anticoagulant Therapy with the endogenous Thrombin Potential....Pages 95-100
Front Matter....Pages 101-101
First thromboembolic Onset in Children carrying either the heterozygeous Factor V G1691A Mutation or the Prothrombin G20210A Variant....Pages 103-110
UFH Bolus Administration in Comparison to subcutaneous Low Molecular Weight Heparin in pediatric cardiac Catheterization....Pages 111-114
Incidence of Inhibitor Development in consecutively recruited severe Hemophilia A and B Patients — a retrospective Single Centre Study....Pages 115-119
Front Matter....Pages 121-121
Factor V Inhibitor and Anti-Phospholipid Antibodies after Treatment with Ciprofloxacin....Pages 123-126
Isolated molecular Defects of von Willebrand Factor Binding to Collagen do not correlate with Bleeding Symptoms....Pages 127-130
Effects of Tissue Factor Pathway Inhibitor and Antithrombin on Thrombin Generation in Tissue Factor-activated Cord Plasma....Pages 131-137
Early and rapid Diagnosis of acute TTP by Measuring Activity of von-Willebrand Factor cleaving Metalloprotease (ADAMTS13): A Case Report....Pages 138-143
Prions and the Safety of Plasma Proteins: Preventive Measures and Research Activities....Pages 144-146
Front Matter....Pages 147-147
Transmission of Parvovirus B19 by Heat-treated Coagulation Factor Concentrates....Pages 149-154
Course of a severe Hemophilia A. Successful Immune Tolerance Therapy (ITT) ten Years after Inhibitor Development....Pages 155-157
Increased Resistance to activated Protein C and Protein C Deficiency in the same Family....Pages 158-163
A Life-threatening Cardiomyopathy following Port-a-Cath Infection under Immune Tolerance Therapy....Pages 164-167
Therapy and Prophylaxis of Bleeding Symptoms in a Patient with Acquired Factor X-Deficiency due to Systemic Amyloidosis (AL-Amyloidosis)....Pages 168-170
Is there a Correlation between vWF-cleaving Protease-Activity, vWF:Ag, Clinical Course and Number of Relapses in 15 Patients with TTP?....Pages 171-176
Life-Threatening Hemorrhage in a Patient with Red Cell Antibodies — Effective Blood Coagulation with rFVIIa....Pages 177-179
Liver Transplantation in a HIV/HCV coinfected Hemophilia A Patient....Pages 180-182
Dysfibrinogenemia following after Snake Bite....Pages 183-187
Bleeding Complication following Tooth Extraction in a Hemophilia A Patient with Inhibitor — A Case Report....Pages 188-191
Cerebral Sinus Thrombosis: Recanalization after intravenous Dalteparin Administration....Pages 192-196
Treatment of FVIII-Autoantibodies by Protein A-based Immunoadsorption and Immunosuppression: A Regimen without FVIII Substitution....Pages 199-202
Factor XI Deficiency caused by a hitherto unknown Mutation in the Factor XI Gene....Pages 203-210
Polymorphisms in FV Gene associated with FV Deficiency — First Results....Pages 211-215
Influence of Phospholipids of the Platelet Membrane of Newborns on the Thrombin Generation....Pages 216-220
Socio-economic Evaluation of Hemophilia Assistance....Pages 221-224
Aspects regarding Locomotor Rehabilitation of Hemophiliacs....Pages 225-229
Prothrombin and Factor VII Genotypes and Phenotypes in healthy Individuals — Results from the Lugen Study....Pages 233-239
Factor V Leiden and other thrombotic risk factors in CHD and myocardial Infarction....Pages 240-246
In vitro Effects of combined Administration of Eptifibatide and Anticoagulants on Thrombin induced Platelet Aggregation after high versus low Coagulant Activation of Platelet Rich Plasma....Pages 247-259
Front Matter....Pages 147-147
Cardiac and cerebral Manifestations of the Antiphospholipid Syndrome....Pages 260-265
Inactivation of Animal Factor VIII by human Factor VIII Inhibitors: Special Methodological Features in Performing the Factor VIII Assay and the Bethesda Assay....Pages 269-274
Inactivation of Animal Factor VIII by human Factor VIII Inhibitors: Investigation of Plasma from Patients with Inhibitors in congenital Hemophilia A and from Patients with acquired Hemophilia A....Pages 275-279
Factor VIII:C Measurement — Comparison between chromogenic and coagulometric Methods in Hemophilia A-Patients with the B-Domain depleted recombinant F VIII-Preparation ReFacto....Pages 280-283
Functional Assessment of fibrinolytic Resistance in whole Blood....Pages 284-288
Quality Control of Platelet Concentrates during Storage using different Forms of Agitation measuring the Platelet Activation....Pages 291-293
Platelet Activation before and after Cryopreservation of Platelet Concentrates with a new Storage Solution....Pages 294-296
Flow Cytometric Measurement of CD34 + Cells: How reliable are absolute Cell Counts generated by the Integration of Beads?....Pages 297-300
An innovative Approach to Teach and Learn diagnostic Skills and therapeutical Management of Coagulation Disorders: CAMPUS — an interactive, Computer- and Case-based Program....Pages 301-304
Expression of Protease-activated Receptors in Neuroblastoma Cells....Pages 305-311
Back Matter....Pages 313-318